日本小児血液・がん学会https://www.jspho.org/pdf/journal/childhood_leukemia...[PDF]6章 ランゲルハンス細胞組織球症 LCH2018年5月30日 · Langerhans cell histiocytosis : effect on course and outcome. J Pediatr 2012 ; 161 : 129-33, e1-3. 6） Grois N, Fahrner B, Arceci RJ, et al. Central nervous system disease in Langerhans cell histiocy-tosis. J Pediatr 2010 ; 156 : 873-81. 天蓋部を除く頭蓋顔面骨
ScienceDirecthttps://www.sciencedirect.com/science/article/pii/S0025619619302733The Mayo Clinic Histiocytosis Working Group Consensus …2019年10月1日 · Langerhans cell histiocytosis involving the LN alone is rare and may be observed or require localized therapies. 105 Involvement of the LNs as a part of multisystem LCH is seen in approximately 5% to 10% of patients and is thought to represent a higher risk of disease. 11, 22 In contrast, lymphadenopathy is notably common in RDD and is referred ...
Mayo Clinic Proceedingshttps://www.mayoclinicproceedings.org/article/S0025-6196(19)30273-3/fulltextThe Mayo Clinic Histiocytosis Working Group Consensus …2019年8月28日 · Histiocytic neoplasms, a rare and heterogeneous group of disorders, primarily include Erdheim-Chester disease, Langerhans cell histiocytosis, and Rosai-Dorfman disease. Due to their diverse clinical manifestations, the greatest challenge posed by these neoplasms is the establishment of a diagnosis, which often leads to a delay in institution of appropriate therapy.
ScienceDirecthttps://www.sciencedirect.com/science/article/pii/S0738081X1930183XLangerhans cell histiocytosis: A great imitator - ScienceDirect2020年3月1日 · Langerhans cell histiocytosis (LCH) is an uncommon but serious inflammatory neoplasia that affects many organs, including the skin. Though uncommon, it should remain high on a clinician’s differential diagnosis in treatment-resistant cases of conditions, such as seborrheic dermatitis, diaper dermatitis, arthropod bites, and many more.
Naturehttps://www.nature.com/articles/s41572-021-00307-9Histiocytic disorders | Nature Reviews Disease Primers2021年10月7日 · Genes and mutations that have been associated with Langerhans cell histiocytosis (LCH), Erdheim–Chester disease (ECD), Juvenile xanthogranuloma (JXG) and Rosai–Dorfman disease (RDD) (panel a ...
PubMedhttps://pubmed.ncbi.nlm.nih.gov/28613635Langerhans Cell Histiocytosis - PubMed2024年4月18日 · Langerhans cell histiocytosis (LCH) is the most common histiocytic disorder where langerin-positive cells coalesce as granulomatous lesions and deposit in various tissues throughout the body as inflammatory infiltrates. Affected organs include but are not limited to the skin, liver, gastrointestinal tract, and central nervous system (CNS ...